Lipoid proteinosis

a rare disorder with pathognomonic lid lesions

Sharma, Vidushi MD FRCS(Edin)
Kashyap, Seema MD
Betharia, Subhash M MD
Gupta, Somesh MD
Pathak, Harish MD

¹Division of Orbit, Oculoplasty and Reconstructive Surgery, Dr Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences, New Delhi, India
²Division of Ocular Pathology, Dr Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences, New Delhi, India
³Department of Dermatology, Post Graduate Institute, Chandigarh, India

Clinical & Experimental Ophthalmology 32(1):p 110-112, January 2004.

Lipoid proteinosis is a rare disorder seen even more rarely by ophthalmologists. The interesting clinical and histopathological features of this disease are described in a brother and sister who presented predominantly with lid lesions, without any systemic complaints. Knowledge of the typical lid lesions may help to diagnose this disorder.