GERSTMANN-STRÄUSSLER-SCHEINKER DISEASE ASSOCIATED WITH THE PRNP A117V-129V MUTATION: NEUROPATHOLOGY OF AN ASYMPTOMATIC GENE CARRIER AND FIVE CLINICALLY AFFECTED INDIVIDUALS FROM A FAMILY

¹Indiana Alzheimer Disease Center, Department of Pathology & Laboratory Medicine, Department of Neurology, Department of Psychiatry, Indiana University School of Medicine, Indianapolis, IN. ²Mihara Memorial Hospital, Isesaki, Gunma, Japan. ³Center for Biologics Evaluation and Research, Food and Drug Administration, Rockville, MD. ⁴Cognitive Neurology & Alzheimer's Disease Center, Department of Pathology, Northwestern University Feinberg School of Medicine, Chicago, IL. ⁵Alzheimer's Disease Center, Department of Neurology, University of California, Davis, Sacramento, CA.