Neuroleptic Malignant Syndrome Associated With Fahr's Syndrome

INTRODUCTION

Fahr's disease(FD) or Bilateral StriatoPallidoDentate Calcinosis (BSPDC) is a neurological entity characterized clinically by Parkinsonism, chorea, dystonia, ataxia, mental deterioration, seizures and neuropsychiatric features, and pathologically [1] by massive bilateral calcification of the: basal ganglia, sulcal depths of the cerebral cortex, dentate nuclei of the cerebellum, internal capsule and lateral parts of the thalamus. Common clinical features include movement disorders such as parkinsonism, speech disorders, psychiatric disorders, epileptic seizure, dementia, cerebellar or extra-pyramidal dysfunction.[2^,3]. These cases have increased incidence of neuroleptic malignant syndrome (NMS). The present case of ours is a rare presentation of Fahr's disease (Dandy walker malformation with Intracranial Calcinosis) with neuroleptic malignant syndrome in young girl who was on anti psychotics for long time.